Go to JCI Insight
  • About
  • Editors
  • Consulting Editors
  • For authors
  • Publication ethics
  • Publication alerts by email
  • Advertising
  • Job board
  • Contact
  • Clinical Research and Public Health
  • Current issue
  • Past issues
  • By specialty
    • COVID-19
    • Cardiology
    • Gastroenterology
    • Immunology
    • Metabolism
    • Nephrology
    • Neuroscience
    • Oncology
    • Pulmonology
    • Vascular biology
    • All ...
  • Videos
    • Conversations with Giants in Medicine
    • Video Abstracts
  • Reviews
    • View all reviews ...
    • Complement Biology and Therapeutics (May 2025)
    • Evolving insights into MASLD and MASH pathogenesis and treatment (Apr 2025)
    • Microbiome in Health and Disease (Feb 2025)
    • Substance Use Disorders (Oct 2024)
    • Clonal Hematopoiesis (Oct 2024)
    • Sex Differences in Medicine (Sep 2024)
    • Vascular Malformations (Apr 2024)
    • View all review series ...
  • Viewpoint
  • Collections
    • In-Press Preview
    • Clinical Research and Public Health
    • Research Letters
    • Letters to the Editor
    • Editorials
    • Commentaries
    • Editor's notes
    • Reviews
    • Viewpoints
    • 100th anniversary
    • Top read articles

  • Current issue
  • Past issues
  • Specialties
  • Reviews
  • Review series
  • Conversations with Giants in Medicine
  • Video Abstracts
  • In-Press Preview
  • Clinical Research and Public Health
  • Research Letters
  • Letters to the Editor
  • Editorials
  • Commentaries
  • Editor's notes
  • Reviews
  • Viewpoints
  • 100th anniversary
  • Top read articles
  • About
  • Editors
  • Consulting Editors
  • For authors
  • Publication ethics
  • Publication alerts by email
  • Advertising
  • Job board
  • Contact

Citations to this article

The innate immune system in cystic fibrosis lung disease
Robert Bals, … , Daniel J. Weiner, James M. Wilson
Robert Bals, … , Daniel J. Weiner, James M. Wilson
Published February 1, 1999
Citation Information: J Clin Invest. 1999;103(3):303-307. https://doi.org/10.1172/JCI6277.
View: Text | PDF
Perspective Article has an altmetric score of 3

The innate immune system in cystic fibrosis lung disease

  • Text
  • PDF
Abstract

Authors

Robert Bals, Daniel J. Weiner, James M. Wilson

×

Total citations by year

Year: 2022 2021 2020 2019 2018 2017 2016 2014 2013 2012 2011 2010 2009 2008 2007 2006 2005 2004 2003 2002 2001 2000 1999 Total
Citations: 1 4 4 1 6 5 5 5 3 5 4 5 4 8 5 9 11 13 7 9 13 13 8 148
Citation information
This citation data is accumulated from CrossRef, which receives citation information from participating publishers, including this journal. Not all publishers participate in CrossRef, so this information is not comprehensive. Additionally, data may not reflect the most current citations to this article, and the data may differ from citation information available from other sources (for example, Google Scholar, Web of Science, and Scopus).

Citations to this article (148)

Title and authors Publication Year
Surface Hydration Protects Cystic Fibrosis Airways from Infection by Restoring Junctional Networks.
Simonin JL, Luscher A, Losa D, Badaoui M, van Delden C, Köhler T, Chanson M
Cells 2022
Transcriptional analysis of cystic fibrosis airways at single-cell resolution reveals altered epithelial cell states and composition
G Carraro, J Langerman, S Sabri, Z Lorenzana, A Purkayastha, G Zhang, B Konda, CJ Aros, BA Calvert, A Szymaniak, E Wilson, M Mulligan, P Bhatt, J Lu, P Vijayaraj, C Yao, DW Shia, AJ Lund, E Israely, TM Rickabaugh, J Ernst, M Mense, SH Randell, EK Vladar, AL Ryan, K Plath, JE Mahoney, BR Stripp, BN Gomperts
Nature Medicine 2021
Motile cilia and airway disease
M Legendre, LE Zaragosi, HM Mitchison
Seminars in Cell & Developmental Biology 2021
Long-term evolution of the epithelial cell secretome in preclinical 3D models of the human bronchial epithelium
D Sanchez-Guzman, S Boland, O Brookes, CM Cord, RL Kuen, V Sirri, AB Squiban, S Devineau
Scientific Reports 2021
spa Typing and Molecular Characterization of Antimicrobial Resistance in Staphylococcus aureus Strains from Patients with Cystic Fibrosis
ED Tomi, A Bertoncelli, E Sartori, I Unali, A Mazzariol
Microbial Drug Resistance 2021
Targeting the phosphoinositide-3-kinase/protein kinase B pathway in airway innate immunity
I Gopallawa, RJ Lee
World journal of biological chemistry 2020
Microbiome Data Enhances Predictive Models of Lung Function in People With Cystic Fibrosis
CY Zhao, Y Hao, Y Wang, JJ Varga, AA Stecenko, JB Goldberg, SP Brown
The Journal of Infectious Diseases 2020
Cigarillos Compromise the Mucosal Barrier and Protein Expression in Airway Epithelia
SH Abdelwahab, B Reidel, JR Martin, A Ghosh, JE Keating, P Haridass, J Carpenter, GL Glish, R Tarran, CM Doerschuk, M Kesimer
American journal of respiratory cell and molecular biology 2020
Results of a RCT assessing saline and xylitol nasal irrigation for CRS and fatigue in Gulf War illness
D Rabago, T Kille, M Mundt, C Obasi
Laryngoscope Investigative Otolaryngology 2020
ENaC-mediated sodium influx exacerbates NLRP3-dependent inflammation in cystic fibrosis
Thomas Scambler, Heledd Jarosz-Griffiths, Samuel Lara-Reyna, Shelly Pathak, Chi Wong, Jonathan Holbrook, Fabio Martinon, Sinisa Savic, Daniel Peckham, Michael McDermott
eLife 2019
Molecular Biology and Physiology of Volume-Regulated Anion Channel (VRAC).
Osei-Owusu J, Yang J, Vitery MDC, Qiu Z
Current topics in membranes 2018
Cell Volume Control in Healthy Brain and Neuropathologies
Wilson CS, Mongin AA
Current topics in membranes 2018
Water Homeostasis and Cell Volume Maintenance and Regulation
Delpire E, Gagnon KB
Current topics in membranes 2018
Loss of the homeostatic protein BPIFA1, leads to exacerbation of otitis media severity in the Junbo mouse model
A Mulay, DW Hood, D Williams, C Russell, SD Brown, L Bingle, M Cheeseman, CD Bingle
Scientific Reports 2018
CrossTalk proposal: mucosal acidification drives early progressive lung disease in cystic fibrosis: CrossTalk
MF Figueira, MJ Webster, R Tarran
The Journal of Physiology 2018
A review of inflammatory mechanism in airway diseases
P Aghasafari, U George, R Pidaparti
Inflammation Research 2018
TGFβ as a therapeutic target in cystic fibrosis
EL Kramer, JP Clancy
Expert Opinion on Therapeutic Targets 2017
Harnessing Neutrophil Survival Mechanisms during Chronic Infection by Pseudomonas aeruginosa: Novel Therapeutic Targets to Dampen Inflammation in Cystic Fibrosis
BS Marteyn, PR Burgel, L Meijer, V Witko-Sarsat
Frontiers in Cellular and Infection Microbiology 2017
Clinical implications of Pseudomonas aeruginosa location in the lungs of patients with cystic fibrosis
JE Moore, P Mastoridis
Journal of Clinical Pharmacy and Therapeutics 2017
Microbiology of the Upper and Lower Airways in Pediatric Cystic Fibrosis Patients
L Sobin, K Kawai, AL Irace, O Gergin, M Cunningham, GS Sawicki, EA Adil
Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery 2017
Comparison of Oropharyngeal Microbiota from Children with Asthma and Cystic Fibrosis
S Boutin, M Depner, M Stahl, SY Graeber, SA Dittrich, A Legatzki, E von Mutius, M Mall, AH Dalpke
Mediators of Inflammation 2017
Neutrophil elastase and matrix metalloproteinase 12 in cystic fibrosis lung disease
CJ Wagner, C Schultz, MA Mall
Molecular and Cellular Pediatrics 2016
Activity of antimicrobial peptides, alone or combined with conventional antibiotics, against Staphylococcus aureus isolated from the airways of cystic fibrosis patients
K Garbacz, W Kamysz, L Piechowicz
Virulence 2016
Esculentin-1a-derived peptides promote clearance of P. aeruginosa internalized in cystic fibrosis bronchial cells as well as lung cells migration: Biochemical properties and a plausible mode of action
F Cappiello, AD Grazia, SZ Li-av, S Scali, L Ferrera, L Galietta, A Pini, Y Shai, YP Di, ML Mangoni
Antimicrobial agents and chemotherapy 2016
Short Palate, Lung, and Nasal Epithelial Clone 1 Has Antimicrobial and Antibiofilm Activities against the Burkholderia cepacia Complex
S Ahmad, J Tyrrell, WG Walton, A Tripathy, MR Redinbo, R Tarran
Antimicrobial agents and chemotherapy 2016
Activity of antimicrobial peptides, alone or combined with conventional antibiotics, against Staphylococcus aureus isolated from the airways of cystic fibrosis patients
K Garbacz, W Kamysz, L Piechowicz
Virulence 2016
Unbiased Screening of Marine Sponge Extracts for Anti-inflammatory Agents Combined with Chemical Genomics Identifies Girolline as an Inhibitor of Protein Synthesis
SY Fung, V Sofiyev, J Schneiderman, AF Hirschfeld, RE Victor, K Woods, JS Piotrowski, R Deshpande, SC Li, NJ de Voogd, CL Myers, C Boone, RJ Andersen, SE Turvey
ACS chemical biology 2014
Moxifloxacin modulates inflammation during murine pneumonia
C Beisswenger, A Honecker, A Kamyschnikow, M Bischoff, T Tschernig, R Bals
Respiratory Research 2014
T cell unresponsiveness in a pediatric cystic fibrosis patient: a case report
R Kushwah, S Gagnon, NB Sweezey
Allergy Asthma & Clinical Immunology 2014
Chronic pulmonary pseudomonal infection in patients with cystic fibrosis: A model for early phase symbiotic evolution
X Qin
Critical Reviews in Microbiology 2014
Lack of Neutrophil Elastase Reduces Inflammation, Mucus Hypersecretion, and Emphysema, but Not Mucus Obstruction, in Mice with Cystic Fibrosis–like Lung Disease
S Gehrig, J Duerr, M Weitnauer, CJ Wagner, SY Graeber, J Schatterny, S Hirtz, A Belaaouaj, AH Dalpke, C Schultz, MA Mall
American journal of respiratory and critical care medicine 2014
CFTR activity and mitochondrial function
AG Valdivieso, TA Santa-Coloma
Redox Biology 2013
Effect of multi-walled carbon nanotube surface modification on bioactivity in the C57BL/6 mouse model
TM Sager, MW Wolfarth, M Andrew, A Hubbs, S Friend, T Chen, DW Porter, N Wu, F Yang, RF Hamilton, A Holian
Nanotoxicology 2013
The Role of Human Beta-Defensin-2 in Pseudomonas aeruginosa Pulmonary Infection in Cystic Fibrosis Patients
D Dalcin, M Ulanova
Infectious Diseases and Therapy 2013
Targeting cytosolic proliferating cell nuclear antigen in neutrophil-dominated inflammation
AD Chiara, M Pederzoli-Ribeil, PR Burgel, C Danel, V Witko-Sarsat
Frontiers in immunology 2012
Innate immunity in cystic fibrosis lung disease
D Hartl, A Gaggar, E Bruscia, A Hector, V Marcos, A Jung, C Greene, G McElvaney, M Mall, G Döring
Journal of Cystic Fibrosis 2012
Serum galactomannan in cystic fibrosis patients colonized with Aspergillus species
TA Warren, Y Yau, F Ratjen, E Tullis, V Waters
Medical Mycology 2012
Low sphingosine-1-phosphate impairs lung dendritic cells in cystic fibrosis
Y Xu, A Krause, M Limberis, TS Worgall, S Worgall
American journal of respiratory cell and molecular biology 2012
Prevalence of streptococci and increased polymicrobial diversity associated with cystic fibrosis patient stability
LM Filkins, TH Hampton, AH Gifford, MJ Gross, DA Hogan, ML Sogin, HG Morrison, BJ Paster, GA O'Toole
Journal of bacteriology 2012
Adhesion of Stenotrophomonas maltophilia to mouse tracheal mucus is mediated through flagella
AK Zgair, S Chhibber
Journal of Medical Microbiology 2011
Evaluation of the Ability of LL-37 to Neutralise LPS In Vitro and Ex Vivo
A Scott, S Weldon, PJ Buchanan, B Schock, RK Ernst, DF McAuley, MM Tunney, CR Irwin, JS Elborn, CC Taggart
PloS one 2011
Antimicrobial peptides: key components of the innate immune system
M Pasupuleti, A Schmidtchen, M Malmsten
Critical Reviews in Biotechnology 2011
Antibiotic Discovery and Development
TJ Dougherty, MJ Pucci
2011
Phylogenetic and metabolic diversity of bacteria associated with cystic fibrosis
AM Guss, G Roeselers, IL Newton, CR Young, V Klepac-Ceraj, S Lory, CM Cavanaugh
The ISME Journal 2010
N-Glycosylation Augmentation of the Cystic Fibrosis Epithelium Improves Pseudomonas aeruginosa Clearance
AT Martino, C Mueller, S Braag, PE Cruz, M Campbell-Thompson, S Jin, TR Flotte
American journal of respiratory cell and molecular biology 2010
Bacteriophage-derived enzyme that depolymerizes the alginic acid capsule associated with cystic fibrosis isolates of Pseudomonas aeruginosa
T Glonti, N Chanishvili, PW Taylor
Journal of Applied Microbiology 2010
Elevated expression of both mRNA and protein levels of IL-17A in sputum of stable Cystic Fibrosis patients
A Decraene, A Willems-Widyastuti, A Kasran, KD Boeck, DM Bullens, LJ Dupont
Respiratory Research 2010
Molecular Basis of Pulmonary Disease
FX McCormack, RJ Panos, BC Trapnell
2010
Host defence peptides: antimicrobial and immunomodulatory activity and potential applications for tackling antibiotic-resistant infections
A Nijnik, R Hancock
Emerging Health Threats Journal 2009
Activity of antimicrobial peptides in the presence of polysaccharides produced by pulmonary pathogens
M Benincasa, M Mattiuzzo, Y Herasimenka, P Cescutti, R Rizzo, R Gennaro
Journal of Peptide Science 2009
Molecular Pathology
WB Coleman, GJ Tsongalis
Molecular Pathology 2009
Host defence peptides: antimicrobial and immunomodulatory activity and potential applications for tackling antibiotic-resistant infections
A Nijnik, RE Hancock
Emerging Health Threats Journal 2009
Clinical Immunology
DB Kuhns
Clinical Immunology 2008
Oxidative stress causes IL8 promoter hyperacetylation in cystic fibrosis airway cell models
TR Bartling, ML Drumm
American journal of respiratory cell and molecular biology 2008
KL4-Surfactant (Lucinactant) Protects Human Airway Epithelium from Hyperoxia
Y Zhu, TL Miller, A Chidekel, TH Shaffer
Pediatric Research 2008
Effects of oxygen concentration and exposure time on cultured human airway epithelial cells:
Y Zhu, TL Miller, CJ Singhaus, TH Shaffer, A Chidekel
Pediatric Critical Care Medicine 2008
Roles of Matrix Metalloproteinases on Intracellular Staphylococcus aureus Growth in Bronchial Epithelial Cell
BR Min, YM Lee, JS Park, WI Choi, KY Kwon
Tuberculosis and Respiratory Diseases 2008
Dail and Hammar’s Pulmonary Pathology
JF Tomashefski, PT Cagle, CF Farver, AE Fraire
2008
Cif Is Negatively Regulated by the TetR Family Repressor CifR
DP MacEachran, BA Stanton, GA O'Toole
Infection and immunity 2008
Aspiration, Bronchial Obstruction, Bronchiectasis, and Related Disorders
Tomashefski JF Jr, Dail DH
2008
Beta-D-glucoside utilization by Mycoplasma mycoides subsp. mycoides SC: possible involvement in the control of cytotoxicity towards bovine lung cells
EM Vilei, I Correia, MH Ferronha, DF Bischof, J Frey
BMC Microbiology 2007
Infection bactérienne et mucoviscidose
G Lenoir, S Vrielynck, M Clairicia, DA Fezaa, M Sorin, I Sermet-Gaudelus
Revue Francophone des Laboratoires 2007
Intracellular survival of Burkholderia cenocepacia in macrophages is associated with a delay in the maturation of bacteria-containing vacuoles
J Lamothe, KK Huynh, S Grinstein, MA Valvano
Cellular Microbiology 2007
Aquaporin-8 expression is reduced in ileum and induced in colon of patients with ulcerative colitis
A Zahn, C Moehle, T Langmann, R Ehehalt, F Autschbach, W Stremmel, G Schmitz
World journal of gastroenterology : WJG 2007
Therapie der Krankheiten im Kindes- und Jugendalter
D Reinhardt
2007
The lactoperoxidase system links anion transport to host defense in cystic fibrosis
GE Conner, C Wijkstrom-Frei, SH Randell, VE Fernandez, M Salathe
FEBS Letters 2006
Bronchoscopic assessment of airway retention time of aerosolized xylitol
L Durairaj, S Neelakantan, J Launspach, JL Watt, MM Allaman, WR Kearney, P Veng-Pedersen, J Zabner
Respiratory Research 2006
IL-9 Modulated MUC4 Gene and Glycoprotein Expression in Airway Epithelial Cells
G Damera, B Xia, HR Ancha, GP Sachdev
Bioscience Reports 2006
Inhibition of IL-8 release from CFTR-deficient lung epithelial cells following pre-treatment with fenretinide
RM Vilela, LC Lands, B Meehan, S Kubow
International Immunopharmacology 2006
Mucoviscidose : physiopathologie, génétique, aspects cliniques et thérapeutiques
I Sermet-Gaudelus, G Lenoir, P Berche, C Ricour, F Lacaille, JP Bonnefont, JJ Robert, A Ferroni, A Edelman
EMC - Pédiatrie - Maladies infectieuses 2006
Mucoviscidose ou fibrose kystique du pancréas
I Sermet-Gaudelus, C Silly-Gaillez, G Lenoir
EMC - Traité de médecine AKOS 2006
Host genetic factors and mycobacterial infections: lessons from single gene disorders affecting innate and adaptive immunity
R Doffinger, SY Patel, DS Kumararatne
Microbes and Infection 2006
Treatment of Bronchomalacia in Cystic Fibrosis by Silicone Stent
GN Herlitz, DI Sternberg, R Palazzo, S Arcasoy, JR Sonett
The Annals of Thoracic Surgery 2006
Staphylococcus aureus Escapes More Efficiently from the Phagosome of a Cystic Fibrosis Bronchial Epithelial Cell Line than from Its Normal Counterpart
TM Jarry, AL Cheung
Infection and immunity 2006
Mucin glycosylation changes in cystic fibrosis lung disease are not manifest in submucosal gland secretions
BL Schulz, AJ Sloane, LJ Robinson, LT Sebastian, AR Glanville, Y Song, AS Verkman, JL Harry, NH Packer, NG Karlsson
Biochemical Journal 2005
Sputum Cathelicidin, Urokinase Plasminogen Activation System Components, and Cytokines Discriminate Cystic Fibrosis, COPD, and Asthma Inflammation
W Xiao, YP Hsu, A Ishizaka, T Kirikae, RB Moss
Chest 2005
Antibiotic allergy in cystic fibrosis
JS Parmar, S Nasser
Thorax 2005
Hyperoxia-induced changes in human airway epithelial cells: The protective effect of perflubron
PB Babu, A Chidekel, TH Shaffer
Pediatric Critical Care Medicine 2005
Cystic fibrosis and lipoxins
CL Karp, LM Flick, R Yang, J Uddin, NA Petasis
Prostaglandins, Leukotrienes and Essential Fatty Acids 2005
Overrepresentation of immunostimulatory CpG motifs in Burkholderia genomes
T Coenye, P Vandamme
Journal of Cystic Fibrosis 2005
Differential cytokine profile in children with cystic fibrosis
J Brazova, A Sediva, D Pospisilova, V Vavrova, P Pohunek, M Macek, J Bartunkova, H Lauschmann
Clinical Immunology 2005
Survival and persistence of opportunistic Burkholderia species in host cells
MA Valvano, KE Keith, ST Cardona
Current Opinion in Microbiology 2005
A minor catalase/peroxidase from Burkholderia cenocepacia is required for normal aconitase activity
MD Lefebre, RS Flannagan, MA Valvano
Microbiology 2005
Human Airway Epithelial Cells Sense Pseudomonas aeruginosa Infection via Recognition of Flagellin by Toll-Like Receptor 5
Z Zhang, JP Louboutin, DJ Weiner, JB Goldberg, JM Wilson
Infection and immunity 2005
Réparation et régénération de l’épithélium respiratoire
C Coraux, R Hajj, P Lesimple, E Puchelle
médecine/sciences 2005
Lymphocytes in cystic fibrosis lung disease: a tale of two immunities
RB Moss
Clinical & Experimental Immunology 2004
β-defensins and LL-37 in bronchoalveolar lavage fluid of patients with cystic fibrosis
CI Chen, S Schaller-Bals, KP Paul, U Wahn, R Bals
Journal of Cystic Fibrosis 2004
Safety assessment of inhaled xylitol in mice and healthy volunteers
L Durairaj, J Launspach, JL Watt, TR Businga, JN Kline, PS Thorne, J Zabner
Respiratory Research 2004
Dysregulation of IL-2 and IL-8 production in circulating T lymphocytes from young cystic fibrosis patients
C Hubeau, RL Naour, M Abély, J Hinnrasky, M Guenounou, D Gaillard, E Puchelle
Clinical & Experimental Immunology 2004
Chronic Pseudomonas aeruginosa infection in cystic fibrosis airway disease: metabolic changes that unravel novel drug targets
SS Yoon, DJ Hassett
Expert Review of Anti-infective Therapy 2004
Anti-neutrophil cytoplasmatic antibodies and lung disease in cystic fibrosis
L Dorlöchter, M Carlsson, EJ Olafsdottir, OD Røksund, K Rosendahl, G Fluge
Journal of Cystic Fibrosis 2004
Protein composition of apical surface fluid from the human airway cell line Calu-3: effect of ion transport mediators
PB Babu, A Chidekel, TH Shaffer
Clinica Chimica Acta 2004
Airway Inflammation and Infection in Congenital Bilateral Absence of the Vas Deferens
M Gilljam, Y Moltyaner, GP Downey, R Devlin, P Durie, AM Cantin, J Zielenski, DE Tullis
American journal of respiratory and critical care medicine 2004
Defensins & other peptides
SM Phadke
Pediatric Pulmonology 2004
Host defense in oral and airway epithelia: chromosome 20 contributes a new protein family
CD Bingle, SU Gorr
The International Journal of Biochemistry & Cell Biology 2004
Impaired nitric oxide synthase-2 signaling pathway in cystic fibrosis airway epithelium
S Zheng, W Xu, S Bose, AK Banerjee, SJ Haque, SC Erzurum
American journal of physiology. Lung cellular and molecular physiology 2004
Principles of Molecular Pathology
AA Killeen
2004
Transcriptome Analysis of the Response of Pseudomonas aeruginosa to Hydrogen Peroxide
M Palma, D DeLuca, S Worgall, LE Quadri
Journal of bacteriology 2004
The potential of recombinant surfactant protein D therapy to reduce inflammation in neonatal chronic lung disease, cystic fibrosis, and emphysema
H Clark, K Reid
Archives of disease in childhood 2003
Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis
RL Gibson, JL Burns, BW Ramsey
American journal of respiratory and critical care medicine 2003
Modulation of Pseudomonas aeruginosa gene expression by host microflora through interspecies communication: Modulation of P. aeruginosa by oropharyngeal flora
K Duan, C Dammel, J Stein, H Rabin, MG Surette
Molecular Microbiology 2003
Src Signaling Links Mediators of Inflammation to Cx43 Gap Junction Channels in Primary and Transformed CFTR-Expressing Airway Cells
S Huang, L Jornot, L Wiszniewski, T Rochat, S Suter, JS Lacroix, M Chanson
Cell communication & adhesion 2003
Distinct cytokine production by lung and blood neutrophils from children with cystic fibrosis
H Corvol, C Fitting, K Chadelat, J Jacquot, O Tabary, M Boule, JM Cavaillon, A Clement
American journal of physiology. Lung cellular and molecular physiology 2003
Expression and regulation of antimicrobial peptides in the gastrointestinal tract
RN Cunliffe, YR Mahida
Journal of leukocyte biology 2003
Series introduction: innate host defense of the respiratory epithelium
PS Hiemstra, R Bals
Journal of leukocyte biology 2003
Mucus clearance as a primary defense mechanism for mamalian airways
Michael Knowles, Richard Boucher
Journal of Clinical Investigation 2002
Peripheral decrease and pulmonary homing of CD4+CD45RO+ helper memory T cells in cystic fibrosis
M Häusler, K Schweizer, S Biesterfeld, T Opladen, G Heimann
Respiratory Medicine 2002
Cystic fibrosis:
AL Brennan, DM Geddes
Current Opinion in Infectious Diseases 2002
Fibrosis quística. Fisiopatología, genética, aspectos clínicos y terapéuticos
I Sermet-Gaudelus, G Lenoir, P Berche, C Ricour, F Lacaille, JP Bonnefont, JJ Robert, A Ferroni, A Edelman
EMC - Pediatría 2002
In vivo airway surface liquid Cl- analysis with solid-state electrodes
Ray A Caldwell, Barbara R Grubb, Robert Tarran, Richard C Boucher, Michael R Knowles, Pierre M Barker
The Journal of General Physiology 2002
Correction of CFTR malfunction and stimulation of Ca2+-activated Cl− channels restore HCO secretion in cystic fibrosis bile ductular cells
A Zsembery
Hepatology 2002
Persistent and aggressive bacteria in the lungs of cystic fibrosis children
CA Hart, C Winstanley
British Medical Bulletin 2002
Human Toll-like receptor 4 recognizes host-specific LPS modifications
AM Hajjar, RK Ernst, JH Tsai, CB Wilson, SI Miller
Nature Immunology 2002
Toll-Like Receptor 4 Mediates Innate Immune Responses to Haemophilus influenzae Infection in Mouse Lung
X Wang, C Moser, JP Louboutin, ES Lysenko, DJ Weiner, JN Weiser, JM Wilson
Journal of immunology (Baltimore, Md. : 1950) 2002
Aerosol and Lobar Administration of a Recombinant Adenovirus to Individuals with Cystic Fibrosis. I. Methods, Safety, and Clinical Implications
PM Joseph, BP O'Sullivan, A Lapey, H Dorkin, J Oren, R Balfour, MA Perricone, M Rosenberg, SC Wadsworth, AE Smith, JA st. George, DP Meeker
Human Gene Therapy 2001
Quantitative analysis of inflammatory cells infiltrating the cystic fibrosis airway mucosa
C Hubeau, M Lorenzato, JP Couetil, D Hubert, D Dusser, E Puchelle, D Gaillard
Clinical & Experimental Immunology 2001
Biology of respiratory epithelial cells: Role in defense against infections
AM Cantin
Pediatric Pulmonology 2001
Le concept d'antibiothérapie inhalée dans la mucoviscidose. À propos d'une forme galénique adaptée de la tobramycine
I Sermet-Gaudelus, D Hubert, D Turck
Archives de Pédiatrie 2001
Distinct pattern of immune cell population in the lung of human fetuses with cystic fibrosis
C Hubeau, E Puchelle, D Gaillard
Journal of Allergy and Clinical Immunology 2001
Salt-independent abnormality of antimicrobial activity in cystic fibrosis airway surface fluid
R Bals, DJ Weiner, RL Meegalla, F Accurso, JM Wilson
American journal of respiratory cell and molecular biology 2001
Antibacterial Activity of Apical Surface Fluid from the Human Airway Cell Line Calu-3: Pharmacologic Alteration by Corticosteroids and β 2 -Agonists
Y Zhang, WW Reenstra, A Chidekel
American journal of respiratory cell and molecular biology 2001
In vitro resistance of Burkholderia cepacia complex isolates to reactive oxygen species in relation to catalase and superoxide dismutase production
MA Valvano, MD Lefebre
Microbiology 2001
Peptide Antibiotics: Discovery Modes Of Action And Applications
D Andreu, L Rivas
Peptide Antibiotics: Discovery Modes Of Action And Applications 2001
Exploitation of syndecan-1 shedding by Pseudomonas aeruginosa enhances virulence
PW Park, GB Pier, MT Hinkes, M Bernfield
Nature 2001
Fibrosis quística del páncreas
I Sermet-Gaudelus, C Silly-Gaillez, G Lenoir
EMC - Tratado de Medicina 2001
Cystische Fibrose
D Reinhardt, M Götz, R Kraemer, MH Schöni
2001
Rhesus Monkey ( Macaca mulatta ) Mucosal Antimicrobial Peptides Are Close Homologues of Human Molecules
R Bals, C Lang, DJ Weiner, C Vogelmeier, U Welsch, JM Wilson
Clinical and diagnostic laboratory immunology 2001
Neutrophils: Molecules, Functions and Pathophysiological Aspects
V Witko-Sarsat, P Rieu, B Descamps-Latscha, P Lesavre, L Halbwachs-Mecarelli
Laboratory Investigation 2000
Mouse models of chronic lung infection withPseudomonas Aeruginosa: Models for the study of cystic fibrosis
PK Stotland, D Radzioch, MM Stevenson
Pediatric Pulmonology 2000
Pathophysiology of the intrahepatic biliary epithelium
M Strazzabosco, C Spirli, L Okolicsanyi
Journal of Gastroenterology and Hepatology 2000
The role of the CFTR in susceptibility to Pseudomonas aeruginosa infections in cystic fibrosis
JB Goldberg, GB Pier
Trends in Microbiology 2000
Epithelial antimicrobial peptides in host defense against infection
R Bals
Respiratory Research 2000
The osmolyte xylitol reduces the salt concentration of airway surface liquid and may enhance bacterial killing
J Zabner, MP Seiler, JL Launspach, PH Karp, WR Kearney, DC Look, JJ Smith, MJ Welsh
Proceedings of the National Academy of Sciences 2000
L'antibiothérapie dans la mucoviscidose
I Sermet-Gaudelus, A Ferroni, JL Gaillard, C Silly, C Chretiennot, G Lenoir, P Berche
Archives de Pédiatrie 2000
Oxidants, nitrosants, and the lung
A der Vliet, CE Cross
The American Journal of Medicine 2000
Unusual respiratory bacterial flora in cystic fibrosis: microbiologic and clinical features:
PM Beringer, MD Appleman
Current Opinion in Pulmonary Medicine 2000
Genotype Analysis and Phenotypic Manifestations of Children With Intermediate Sweat Chloride Test Results
P Desmarquest, D Feldmann, A Tamalat, M Boule, B Fauroux, G Tournier, A Clement
Chest 2000
Transplantation and Changing Management of Organ Failure
P Cochat
2000
Role of Cystic Fibrosis Transmembrane Conductance Regulator in Pulmonary Clearance of Pseudomonas aeruginosa In Vivo
ZC Chroneos, SE Wert, JL Livingston, DJ Hassett, JA Whitsett
Journal of immunology (Baltimore, Md. : 1950) 2000
Staphylococcus aureus RN6390 Replicates and Induces Apoptosis in a Pulmonary Epithelial Cell Line
EI Tuomanen, BC Kahl, M Goulian, W van Wamel, M Herrmann, SM Simon, G Kaplan, G Peters, AL Cheung
Infection and immunity 2000
Status of gene therapy for cystic fibrosis lung disease
RC Boucher
Journal of Clinical Investigation 1999
Status of gene therapy for cystic fibrosis lung disease
RC Boucher
Journal of Clinical Investigation 1999
The genesis of cystic fibrosis lung disease
JJ Wine
Journal of Clinical Investigation 1999
Transfer of a cathelicidin peptide antibiotic gene restores bacterial killing in a cystic fibrosis xenograft model
R Bals, DJ Weiner, RL Meegalla, JM Wilson
Journal of Clinical Investigation 1999
Neutrophil antibacterial peptides, multifunctional effector molecules in the mammalian immune system
GH Gudmundsson, B Agerberth
Journal of Immunological Methods 1999
Burkholderia cepacia is resistant to the antimicrobial activity of airway epithelial cells
RM Baird, H Brown, AW Smith, ML Watson
Immunopharmacology 1999
Intracellular survival of Burkholderia cepacia complex isolates in the presence of macrophage cell activation
MA John, MA Valvano, LS Saini, SB Galsworthy
Microbiology 1999
Mining variations in genes of innate and phagocytic immunity: current status and future prospects
C B Foster, S J Chanock
Current Opinion in Hematology 1999

← Previous 1 2 3 4 5 6 Next →

Advertisement

Copyright © 2025 American Society for Clinical Investigation
ISSN: 0021-9738 (print), 1558-8238 (online)

Sign up for email alerts

Mentioned in 1 Q&A threads
131 readers on Mendeley
See more details