Queen's Square, London, described the detailed clinical and pathologic findings of 4
patients, all of whom, he believed, had the same disease. He also included careful
descriptions of 8 similar patients from the literature, in each case pointing out the clinical
features of progressive lenticular degeneration in association with the pathologic findings of
hepatic cirrhosis. 1, 2 Although Wilson believed that hepatic involvement was not a
significant factor in the evolution of the disease, the prominent role of hepatic cirrhosis in the …