Pathogenesis of cystic fibrosis.

C Koch, N Hoiby - The Lancet, 1993 - elibrary.ru
C Koch, N Hoiby
The Lancet, 1993elibrary.ru
Describes cystic fibrosis, the most common serious inherited disease characterized by
malabsorption due to exocrine pancreatic insufficiency, recurrent bacterial infections,
increased salt loss in sweat and male infertility. Cystic fibrosis transmembrane conductance
regulator and genetics; Sweat gland; Respiratory system; Infections of the lower respiratory
tract; Conclusion.
Аннотация
Describes cystic fibrosis, the most common serious inherited disease characterized by malabsorption due to exocrine pancreatic insufficiency, recurrent bacterial infections, increased salt loss in sweat and male infertility. Cystic fibrosis transmembrane conductance regulator and genetics; Sweat gland; Respiratory system; Infections of the lower respiratory tract; Conclusion.
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