[HTML][HTML] Treatment of pachyonychia congenita

LM Milstone, P Fleckman, SA Leachman… - Journal of Investigative …, 2005 - Elsevier
LM Milstone, P Fleckman, SA Leachman, IM Leigh, AS Paller, MAM Van Steensel
Journal of Investigative Dermatology Symposium Proceedings, 2005Elsevier
There are currently no specific treatments for pachyonychia congenita (PC). Available
treatments generally are directed at specific manifestations of the disorder, and an effective
treatment plan must recognize that different patients are more or less troubled by different
manifestations of the disease. Treatment for all aspects of PC has been less than completely
satisfactory. Very few studies have compared different approaches to treatment, and fewer
still have given longitudinal follow-up of efficacy and patient acceptance. This review is …
There are currently no specific treatments for pachyonychia congenita (PC). Available treatments generally are directed at specific manifestations of the disorder, and an effective treatment plan must recognize that different patients are more or less troubled by different manifestations of the disease. Treatment for all aspects of PC has been less than completely satisfactory. Very few studies have compared different approaches to treatment, and fewer still have given longitudinal follow-up of efficacy and patient acceptance. This review is essentially a compilation of anecdotes. It was collected from physicians' reports in the literature, from direct communication with physicians currently following patients with PC and from patients who answered a questionnaire on the Pachyonychia Congenita Project web page (http://www.pachyonychia.org/Registry.html).
Elsevier